Abstract: Congenital chylous ascites is a rare disease in infants and young children,which is characterized with milky white ascites,but as a result of the relevant reports and study is less,and the lack of standardized diagnosis and treatment standards,clinical practitioners don't understand it deeply,and children can't get timely and effective treatment,which not only cause the prolonged course of the disease,but also bring great worries and troubles to parents and children.In severe cases,the children can die.In this paper,combined with the existing literature,the pathogenesis,clinical manifestations,diagnostic examination and treatment of congenital chylous ascites are systematically summarized,so as to provide clinicians with a perfect basis for the treatment of congenital chylous ascites,and provide suggestions for refractory chylous ascites,amd promote the early recovery of children.

Key words: congenital, chylous ascites, causes, diagnosis, treatment